The butterfly disease: symptoms and treatments

Epidermolysis bullosa or butterfly disease, — a rare and dangerous disease. It is a genetic form of dermatitis, which is characterized by inborn defects in the structure of the skin. Unfortunately, to date there is no effective treatment of such disorders.

Butterfly Disease: causes and symptoms. As already mentioned, this disease is hereditary and manifests as a rule, immediately after birth. What is this disease? First we need to consider the structure of the skin of a normal person.

In humans, the top layer of skin, or epidermis, is designed to protect from the influence of the external environment. He is in good condition connects with the deep ball — the dermis. Patients with a diagnosis of ‘butterfly disease” the connection between the epidermis and dermis are missing or not strong enough to hold all the layers of skin together. That is why the skin is such a child prone to injury.

Congenital epidermolysis bullosa manifests itself immediately after birth. Appear on the skin wounds and sores, even from the slightest external influence. If the child something concerns, then the skin appears immediately trail. Of course, the butterfly disease is accompanied by persistent pain.

As the disease affects also the mucous membranes of the eyes, oral cavity, larynx, because of which the child becomes difficult to eat. In a later stage may experience loss of teeth, damage to the mucous membranes of the esophagus and intestines.

Of Course, by itself, the butterfly disease is not fatal. But to live in this state it is difficult. In addition, permanent wounds, poorly healing ulcers and blisters are the perfect gateway for fungal, bacterial and viral infections. In the absence of necessary care there is sepsis and the emergence of foci of necrosis.

Epidermolysis Bullosa: treatment methods. Unfortunately, to date the disease is incurable. The main treatment methods are intended to prevent infection and development of sepsis.

In some cases, the child needs regular therapy with glucocorticoid hormones. Such a treatment helps to prevent the rash and blistering on the skin, mucous membranes of internal organs. Sometimes conduct and treatment with immunomodulators, which help the body to fight infections.

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For a sick child needs permanent care, which includes regular disinfection of wounds and dressings. Wounds treated with olive oil solutions of vitamins, ointments with antibiotics, infusions of medicinal herbs. Very useful for sore skin is a therapeutic bath with a decoction of oak bark, succession, chamomile or a weak solution of potassium permanganate.

Special attention should be paid to food. In the first months of life breastfeeding is necessary. In the future, food should be liquid, without salt, spices or any irritating ingredients. After feeding the baby must rinse your mouth with warm, water digested — this will prevent the appearance of bubbles and suppuration of the gums.

Shoes and clothing should be as soft and made exclusively from natural fabrics. If the bones are not deformed, the child needs to move — this will help to prevent the appearance of contractures.

The butterfly Disease is often accompanied by the development of anemia, which for a sick child is extremely dangerous. It is therefore necessary continuous monitoring blood condition and, if necessary — the transfusion of plasma and albumin.

Sometimes used in the treatment of "Tocopherol acetate" — a drug that stimulates the production of elastic and collagen fibers of the dermis. Therapy takes place in several stages and involves several repeated courses. For some patients this treatment has become salvation.

In any case, the butterfly disease — a very serious disease that needs constant treatment.